A 12½ years old boy presented with recurrent seizures,
which had started since 7 months of age and gradually
became more frequent and difficult to control. On
examination the boy was found apathetic, noncommunicating
and severely mentally retarded. He had
frequent myoclonic seizures, which involved all 4 limbs
lasting for 15-20seconds.On skin survey there were
multiple tiny red nodular angio-fibromas over nose and
cheeks, 4-5 hypomelanotic macules (ash leaf
macule)seen on the back of trunk and thigh. In addition,
fewshagreen patches were also found on back.