Abstract:
Cleidocranial dysplasia (CCD) is an uncommon
autosomal inheritant congenital skeletal defect that
primarily affects the bones and teeth, and shows an
autosomal inheritance. A 13-year-old Bangladeshi
girl presented with delayed eruption of the
permanent anterior teeth. She was short-statured,
well-oriented young girl with narrow, drooped
shoulders, malformed or absent clavicles,
brachycephalic head with frontal and parietal
bossing, hypoplasticzygomatic bones, bulging
calvarium, and depressed nasal bridge with a broad
alar base. Intraoral examination revealed persistence
of the primary dentition, delayed eruption of the
permanent teeth, an Angle class III malocclusion,
negative overjet, bilateral posterior crossbite. This
rarecase of CCD is so far the first case from
Bangladesh to be documented in perspective to
dental surgery and orthodontics.
Key Words: Autosomal InheritanceCleidocranial
Dysplasia, Delayed Eruption,Supernumerary Teeth